What is Cerebral palsy
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Definition
Cerebral palsy is condition, sometimes thought of as a group of disorders that can involve brain and nervous system functions such as movement, learning, hearing, seeing, and thinking.
Ther are several different types of cerebral palsy, including spastic, dyskinetic, ataxic, hypotonic, and mixed.
Alternative Names
Spastic paralysis; Paralysis - spastic; Spastic hemiplegia; Spastic diplegia; Spastic quadriplegia
Causes
Cerebral palsy is caused by injuries or abnormalities of the brain. Most of these problems occur as the baby grows in the womb, but they can happen at any time during the first 2 years of life, while the baby's brain is still developing.
In some people with cerebral palsy, parts of the brain are injured due to low levels of oxygen (hypoxia) in the area. It is not known why this occurs.
Premature infants have a slightly higher risk of developing cerebral palsy. Cerebral palsy may also occur during early infancy as a result of several conditions, including:
Bleeding in the brain
Brain infections (encephalitis, meningitis, herpes simplex infections)
Head injury
Infections in the mother during pregnancy (rubella)
Severe jaundice
In some cases the cause of cerebral palsy is never determined.
Symptoms
Symptoms of cerebral palsy can be very different between people with this group of disorders. Symptoms may:
Be very mild or very severe
Only involve one side of the body or both sides
Be more pronounced in either the arms or legs, or involve both the arms and legs
Symptoms are usually seen before a child is 2 years old, and sometimes begin as early as 3 months. Parents may notice that their child is delayed in reaching, and in developmental stages such as sitting, rolling, crawling, or walking.
There are several different types of cerebral palsy. Some people have a mixture of symptoms.
Symptoms of spastic cerebral palsy, the most common type, include:
Muscles that are very tight and do not stretch. They may tighten up even more over time.
Abnormal walk (gait): arms tucked in toward the sides, knees crossed or touching, legs make "scissors" movements, walk on the toes
Joints are tight and do not open up all the way (called joint contracture)
Muscle weakness or loss of movement in a group of muscles (paralysis)
The symptoms may affect one arm or leg, one side of the body, both legs, or both arms and legs
The following symptoms may occur in other types of cerebral palsy:
Abnormal movements (twisting, jerking, or writhing) of the hands, feet, arms, or legs while awake, which gets worse during periods of stress
Tremors
Unsteady gait
Loss of coordination
Floppy muscles, especially at rest, and joints that move around too much
Other brain and nervous system symptoms:
Decreased intelligence or learning disabilities are common, but intelligence can be normal
Speech problems (dysarthria)
Hearing or vision problems
Seizures
Pain, especially in adults (can be difficult to manage)
Eating and digestive symptoms
Difficulty sucking or feeding in infants, or chewing and swallowing in older children and adults
Problems swallowing (at all ages)
Vomiting or constipation
Other symptoms:
Increased drooling
Slower than normal growth
Irregular breathing
Urinary incontinence
Exams and Tests
A full neurological exam is critical. In older people, testing cognitive function is also important.
The following other tests may be performed:
Blood tests
CT scan of the head
Electroencephalogram (EEG)
Hearing screen
MRI of the head
Vision testing
Treatment
There is no cure for cerebral palsy. The goal of treatment is to help the person be as independent as possible.
Treatment requires a team approach, including:
Primary care doctor
Dentist (dental check-ups are recommended around every 6 months)
Social worker
Nurses
Occupational, physical, and speech therapists
Other specialists, including a neurologist, rehabilitation physician, pulmonologist, and gastroenterologist
Treatment is based on the person's symptoms and the need to prevent complications.
Self and home care include:
Getting enough food and nutrition
Keeping the home safe
Performing exercises recommended by the health care providers
Practicing proper bowel care (stool softeners, fluids, fiber, laxatives, regular bowel habits)
Protecting the joints from injury
Putting the child in regular schools is recommended, unless physical disabilities or mental development makes this impossible. Special education or schooling may help.
The following may help with communication and learning:
Glasses
Hearing aids
Muscle and bone braces
Walking aids
Wheelchairs
Physical therapy, occupational therapy, orthopedic help, or other treatments may also be needed to help with daily activities and care.
Medications may include:
Anticonvulsants to prevent or reduce the frequency of seizures
Botulinum toxin to help with spasticity and drooling
Muscle relaxants (baclofen) to reduce tremors and spasticity
Surgery may be needed in some cases to:
Control gastroesophageal reflux
Cut certain nerves from the spinal cord to help with pain and spasticity
Place feeding tubes
Release joint contractures
Stress and burnout among parents and other caregivers of cerebral palsy patients is common, and should be monitored.
Support Groups
For organizations that provide support and additional information, see cerebral palsy resources.
Outlook (Prognosis)
Cerebral palsy is a lifelong disorder. Long-term care may be required. The disorder does not affect expected length of life. The amount of disability varies.
Many adults are able to live in the community, either independently or with different levels of help. In severe cases, the person may need to be placed in an institution.
Possible Complications
Bone thinning or osteoporosis
Bowel obstruction
Hip dislocation and arthritis in the hip joint
Injuries from falls
Joint contractures
Pneumonia caused by choking
Poor nutrition
Reduced communication skills (sometimes)
Reduced intellect (sometimes)
Scoliosis
Seizures (in about half of patients)
Social stigma
When to Contact a Medical Professional
Call your health care provider if symptoms of cerebral palsy develop, especially if you know that an injury occurred during birth or early infancy.
Prevention
Getting the proper prenatal care may reduce the risk of some rare causes of cerebral palsy. However, dramatic improvements in care over the last 15 years have not reduced the rate of cerebral palsy. In most cases, the injury causing the disorder may not be preventable.
Pregnant mothers with certain medical conditions may need to be followed in a high-risk prenatal clinic.
References
Johnston MV. Encephalopathies. In: Kliegman RM, Behrman RE, Jenson HB, Stanton BF, eds. Nelson Textbook of Pediatrics. 18th ed. Philadelphia, Pa: Saunders Elsevier; 2007: chap 598.
Whelan MA. Practice parameter: diagnostic assessment of the child with cerebral palsy: report of the Quality Standards Subcommittee of the American Academy of Neurology and the Practice Committee of the Child Neurology Society. Neurology. 2004;63:1985-1986.
Reid SM, Johnstone BR, Westbury C, Rawicki B, Reddihough DS. Randomized trial of botulinum toxin injections into the salivary glands to reduce drooling in children with neurological disorders. Dev Med Child Neurol. 2008;50:123-126.
Sakzewski L, Ziviani J, Boyd R. Systematic review and meta-analysis of therapeutic management of upper-limb dysfunction in children with congenital hemiplegia. Pediatrics. 2009;123:e1111-1122.
Reviewed By: Daniel B. Hoch, PhD, MD, Assistant Professor of Neurology, Harvard Medical School, Department of Neurology, Massachusetts General Hospital; and Neil K. Kaneshiro, MD, MHA, Clinical Assistant Professor of Pediatrics, University of Washington School of Medicine. Also reviewed by David Zieve, MD, MHA, Medical Director, A.D.A.M., Inc.
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